PLAIN RADIOGRAPHIC DIAGNOSIS OF CONGENITAL HEART DISEASE

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4I-1. Idiopathic pulmonary artery dilation. (Legend.)

A. The heart is normal size with a convex prominent pulmonary artery and normal size branch pulmonary arteries. In this condition the prominent pulmonary artery resembles that of pulmonary valvular stenosis but hemodynamic studies are normal. It may not be possible to radiographically distinguish idiopathic pulmonary artery dilation, pulmonary valvular stenosis and a small atrial septal defect.

B. Catheter is coiled in dilated pulmonary artery.

4i1b.jpg (79457 bytes)

Idiopathic pulmonary artery dilation

Clinically idiopathic pulmonary artery dilation is very similar to pulmonary valve stenosis with features of an ejection click, widely split second heart sound, and radiographic features of a dilated main pulmonary artery segment. Echocardiogram in these patients however demonstrates a normally appearing pulmonary valve.