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H , 0޽h ? ff>>\`Y{ff___PPT10i.\+D=' = @B +"F0 MEp0(  0 0  x0e0e?Rectangle 2 `}   J>5 years    0  x0e0e?Rectangle 3 `   Visits Q6-12 months CBC at least yearly UA at least yearly BUN, Cr and LFTs every 2-3 years Flu vaccine yearly Consider stop PCN VK NOT if pt has had splenectomy OR h/o invasive pneumococcal infxn Continue folic acid Annual eye exam starting at 10 yrs (focus on retina) PA PI P H(A5 H 0 0޽h ? ff>>\`Y{ff___PPT10i.ar+D=' = @B +"N0 UM4(  4 4  x0e0e?Rectangle 2 `}   HGrowth   4  x@0e0e?Rectangle 3 `  3Decrease in height and weight compared to peers During adolescent growth spurt begin to catch up with peers Do NOT experience growth failure, only growth delay Delayed puberty Menarche delayed 2-2.5 years Dysmenorrhea may precipitate pain episodes Puberty, although delayed, proceeds normally once startedd0 Zr Z Z Z0r 4H 4 0޽h ? ff>>\`Y{ff___PPT10i.qV+D=' = @B +"0 8/(  8 8  x0e0e?Rectangle 2 `}   M Adolescence    8  x0e0e?Rectangle 3 `  Visits annually CBC yearly UA yearly BUN, Cr and LFTs every 2-3 years Ferritin or serum iron and TIBC at least once Flu vaccine yearly Transition from pediatric to adult care. Zd; H 8 0޽h ? ff>>\`Y{ff___PPT10i.@V+D=' = @B +"30 :2<(  < <  x\0e0e?Rectangle 2 `}   GAdult  w <  x0e0e?Rectangle 3 `  5Biannual visit for pt >30 years Annual eye exam Vaccinations Hepatitis vaccine Pneumococcal vaccine (Pneumovax) Evaluate for elevated BP and pulmonary HTN Foot care and protective shoes Consider PCN VK prophylaxis Folic acid daily to ensure adequate amounts for high erythrocyte turnover Consider hydroxyurea H= P3 P P=3 6H < 0޽h ? ff>>\`Y{ff___PPT10i.@+U+D=' = @B +"0 @Y(  @ @  xt0e0e?Rectangle 2 `}   K Pneumovax    @  x$0e0e?Rectangle 3 `  6First dose at 2 years If pt <10 years, then give booster at age 3-5 years If pt >10 years, then give booster 5 years after first dose Support for a one time booster 5 years after first dose; some institutions give Q5 years* Y Y H @ 0޽h ? ff>>\`Y{ff___PPT10i. -+D=' = @B +"0 D6(  D D  px0e0e?Title 1 `}   PBlood Pressure   D   0e0e?,Content Placeholder 2 `  Pt with SCD-SS have lower systolic and diastolic blood pressure compared to others Modest increases in BP within the normal range for general population may indicate underlying renal dz  H D 0޽h ? ff>>\`Y{ff___PPT10i.+D=' = @B +"b0 iaH(  H$ H  xH0e0e?Rectangle 2 `}   XPulmonary Hypertension   H  x0e0e?Rectangle 3 `  qMonitor for pulmonary hypertension Unexplained dyspnea or hypoxemia Loud P2 Enlarged heart (RV) on CXR Check Echo*# O #O rH H 0޽h ? ff>>\`Y{ff___PPT10i.PW+D=' = @B +"90 @8L(  L  L  x$0e0e?Rectangle 2 `}   TPCN VK prophylaxis  p L  x)0e0e?Rectangle 3 `  JBy age 2 months, start PCN VK 125 mg po BID Age 3 years increase dose to PCN VK 250 mg po BID Functional asplenia occurs <1 year age in pt with SCD-SS and SCD SB0thal SCD-SS patients have usually infarcted their spleens before 4 years Can be discontinued after age 5 years except in child who has had splenectomy or invasive infxn,K   KH L 0޽h ? ff>>\`Y{ff___PPT10i.`#O+D=' = @B +"E0 LDP(  P P  x$?0e0e?Rectangle 2 `}   M Hydroxyurea    P  x@0e0e?Rectangle 3 `  uIncreases Hb F levels Improves red cell deformability and hydration Reduces red cell adhesion to vascular endotheliumv v vH P 0޽h ? ff>>\`Y{ff___PPT10i.@9+D=' = @B +"0 Tk(  T T  pI0e0e?Title 1 `}   SBlood Transfusion   T  PN0e0e?,Content Placeholder 2 `  .Post-transfusion, Hb level should not exceed 10-11 g/dL Check for infection: HIV, Hepatitis panel Alloimmunization in up to 30% of pt who receive frequent transfusions Volume overload Iron overload Use of chelator Exchange transfusion* % % H T 0޽h ? ff>>\`Y{ff___PPT10i.+D=' = @B +"k0 rjX(  X X  x`Z0e0e?Rectangle 2 `}   RClinical Case #1   X  xa0e0e?Rectangle 3 `  2 yo AAM with h/o SCD-SS presents for sick visit. On physical exam pt has palpable spleen not previously observed. Pt s baseline Hb ~8 but current Hb ~3 Reticulocyte count increased from pt s baseline   H X 0޽h ? ff>>\`Y{ff___PPT10i.+D=' = @B +"0 wo \(  \ \  x\j0e0e?Rectangle 2 `}   RClinical Case #1   \  xn0e0e?Rectangle 3"PK![Content_Types].xml|N0 HC+jS8 @:Q۸ ??\o<7p]V޷O(I'6E=, ){Ō4>I)q7UuDހǏ)}nL"Mᴸ&g0eSA)΄2';2 WYu7{ɯΒzŘqFrj9K*(]mOlPK!Z,[ _rels/.relslj0 ``t_Pƈ[>,dgzjǎ?I'f#®Pb-\/Ƿ0Z]nLnp__3.iJV KQBiDžrL,Vʌ/7р4`ANar+m;E/'3U Aںv83/PK!jdrs/downrev.xmlDMk1EBCxwQёQĶP)]?'ϙ$7t./r.gt.䃲Fh#SYL-|́Fbk QBګek &(!ahS5 [>βרLzhѦ\}z{\O妴m}ʻ.D[?/_ԫ0ga$dL/PK-![Content_Types].xmlPK-!Z,[ _rels/.relsPK-!jdrs/downrev.xmlPK `H$D 0  FWhat medical condition do you suspect? Acute Splenic Sequestration Crisis: sudden enlargement of spleen, precipitous fall in Hct (at least 2 g/DL), rise in reticulocyte count. What is most common age for this to develop? Often occurs between 6 months and 3 years Hb SS at age <3 years. Variants at any time during childhood.T'  - i '-i GH \ 0޽h ? ff>>\`Y{ff ___PPT10 . w$+qZD ' = @B Ds ' = @BA?%,( < +O%,( < +Dn' =%(D' =%(D' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*\'%(D' =+4 8?\CB#ppt_xBCB#ppt_xB*Y3>B ppt_x<*\'D' =+4 8?dCB1+#ppt_h/2BCB#ppt_yB*Y3>B ppt_y<*\'D4' =%(D' =%(D' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*\%(D' =+4 8?\CB#ppt_xBCB#ppt_xB*Y3>B ppt_x<*\D' =+4 8?dCB1+#ppt_h/2BCB#ppt_yB*Y3>B ppt_y<*\D' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*\G%(D' =+4 8?\CB#ppt_xBCB#ppt_xB*Y3>B ppt_x<*\GD' =+4 8?dCB1+#ppt_h/2BCB#ppt_yB*Y3>B ppt_y<*\G+"p0 0`(  ` `  x0e0e?Rectangle 2 `}   RClinical Case #1  L `  xh0e0e?Rectangle 3"PK![Content_Types].xml|N0 HC+jS8 @:Q۸ ??\o<7p]V޷O(I'6E=, ){Ō4>I)q7UuDހǏ)}nL"Mᴸ&g0eSA)΄2';2 WYu7{ɯΒzŘqFrj9K*(]mOlPK!Z,[ _rels/.relslj0 ``t_Pƈ[>,dgzjǎ?I'f#®Pb-\/Ƿ0Z]nLnp__3.iJV KQBiDžrL,Vʌ/7р4`ANar+m;E/'3U Aںv83/PK!Y{cdrs/downrev.xmlDN@EM͘&[-VBP ݡvw;A'grntޛVȇYV > jl% 0]_M1lwtJĆ 1v`,#妕I( 6jhYS6 qMeҼaQ_<ܭU5 qu9F0D kPK-![Content_Types].xmlPK-!Z,[ _rels/.relsPK-!Y{cdrs/downrev.xmlPK `H$@ 0  kWhat treatment do you recommend? Hospitalization IVF +- blood transfusion After first or second crisis, consider elective splenectomy when child is stable Preventive education: Caretaker should know how to palpate for splenic size and know about risk of sequestration crisis*!  ! H ` 0޽h ? ff>>\`Y{ff  ___PPT10 . +_(DD ' = @B DU ' = @BA?%,( < +O%,( < +D ' =%(D4 ' =%(D1' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*`!1%(D' =-m6Bbox(in)*<3<*`!1D1' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*`1J%(D' =-m6Bbox(in)*<3<*`1JD1' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*`J%(D' =-m6Bbox(in)*<3<*`JD1' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*`%(D' =-m6Bbox(in)*<3<*`+"0 @d(  d d  xH0e0e?Rectangle 2 `}   RClinical Case #2  ! d  x0e0e?Rectangle 3 `  U17 yo AAF with h/o RAD and SCD-SS was recently hospitalized for a vaso-occlusive pain crisis. Presents 1 week after discharge for hospital follow-up. Now c/o minimal bilateral LE pain, chest discomfort, fever (T=100) Pulse ox in the office Sat 88% on RA Chest X-ray: Normal  H d 0޽h ? ff>>\`Y{ff___PPT10i.?+D=' = @B +"0 PhJ(  h h  x0e0e?Rectangle 2 `}   RClinical Case #2   h  xX0e0e?Rectangle 3"PK![Content_Types].xml|N0 HC+jS8 @:Q۸ ??\o<7p]V޷O(I'6E=, ){Ō4>I)q7UuDހǏ)}nL"Mᴸ&g0eSA)΄2';2 WYu7{ɯΒzŘqFrj9K*(]mOlPK!Z,[ _rels/.relslj0 ``t_Pƈ[>,dgzjǎ?I'f#®Pb-\/Ƿ0Z]nLnp__3.iJV KQBiDžrL,Vʌ/7р4`ANar+m;E/'3U Aںv83/PK!?/drs/downrev.xmlDn0xkz+N $ D KבBxZ=ь7_'rv .nRY<@L .a\1[:B%"} LJ_dЏlGuC9M+I25v<nyz\ϊua6aCaz#/M+4|For _ ?PK-![Content_Types].xmlPK-!Z,[ _rels/.relsPK-!?/drs/downrev.xmlPK `H$D 0  What medical condition do you suspect? Acute Chest Syndrome Ages birth-9 years May be accompanied by or preceded by pain the chest or extremities, fever, respiratory distress and low O2 Sat Hypoxemia is not necessary for dx CXR may be normal initially with later development of infiltrate 30% of all Hb SS pt will have one episode of Acute Chest Syndrome; of these pt will have recurrent episodes Asthma increases risk of ACS2' P P' H h 0޽h ? ff>>\`Y{ff___PPT10.+XD' = @B D=' = @BA?%,( < +O%,( < +Dn' =%(D' =%(D' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*h'<%(D' =+4 8?dCB0-#ppt_w/2BCB#ppt_xB*Y3>B ppt_x<*h'<D' =+4 8?\CB#ppt_yBCB#ppt_yB*Y3>B ppt_y<*h'<D ' =%(D ' =%(D1' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*h<O%(D' =-m6Bbox(in)*<3<*h<OD1' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*hO%(D' =-m6Bbox(in)*<3<*hOD1' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*h%(D' =-m6Bbox(in)*<3<*hD1' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*h!%(D' =-m6Bbox(in)*<3<*h!D1' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*h!%(D' =-m6Bbox(in)*<3<*h!D1' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*h%(D' =-m6Bbox(in)*<3<*h+"f0 me`l(  l l  x<0e0e?Rectangle 2 `}   RClinical Case #3   l  x0e0e?Rectangle 3 `  5 yo AAM with SCD-SS disease presents with a new limp What medical conditions would you consider? What other information would you like to know?  H l 0޽h ? ff>>\`Y{ff___PPT10i.jXl+D=' = @B +""0 ppe(  p' p  x0e0e?Rectangle 2 `}   [DDX Limp in Hb SS Disease   p  x0e0e?Rectangle 3"PK![Content_Types].xml|N0 HC+jS8 @:Q۸ ??\o<7p]V޷O(I'6E=, ){Ō4>I)q7UuDހǏ)}nL"Mᴸ&g0eSA)΄2';2 WYu7{ɯΒzŘqFrj9K*(]mOlPK!Z,[ _rels/.relslj0 ``t_Pƈ[>,dgzjǎ?I'f#®Pb-\/Ƿ0Z]nLnp__3.iJV KQBiDžrL,Vʌ/7р4`ANar+m;E/'3U Aںv83/PK!!(drs/downrev.xmlDN@EM1MZR97 8vms;{gbн85QMmUgj "D2zk͆؈1 6FWH5ulR^SL7Ry:&uIMI-9^\ovZ*;)|oD!ڕ/j&&{9}Nm(D/&SPK-![Content_Types].xmlPK-!Z,[ _rels/.relsPK-!!(drs/downrev.xmlPK `H$D 0  DDX Osteomyelitis Avascular Necrosis of the hip Stroke Other information: H/o HA Fever Labs: WBC, ESR Extremity exam, hip exam Neuro examd Z3 Z ZA Z3A H p 0޽h ? ff>>\`Y{ff___PPT10.G+qZD]' = @B D' = @BA?%,( < +O%,( < +Dn' =%(D' =%(D' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*p%(D' =+4 8?\CB#ppt_xBCB#ppt_xB*Y3>B ppt_x<*pD' =+4 8?dCB1+#ppt_h/2BCB#ppt_yB*Y3>B ppt_y<*pDn' =%(D' =%(D' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*p0%(D' =+4 8?\CB#ppt_xBCB#ppt_xB*Y3>B ppt_x<*p0D' =+4 8?dCB1+#ppt_h/2BCB#ppt_yB*Y3>B ppt_y<*p0Dn' =%(D' =%(D' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*p07%(D' =+4 8?\CB#ppt_xBCB#ppt_xB*Y3>B ppt_x<*p07D' =+4 8?dCB1+#ppt_h/2BCB#ppt_yB*Y3>B ppt_y<*p07D ' =%(D ' =%(D9' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*pJQ%(D' =-u6Bdiamond(in)*<3<*pJQD9' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*pQW%(D' =-u6Bdiamond(in)*<3<*pQWD9' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*pWg%(D' =-u6Bdiamond(in)*<3<*pWgD9' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*pg%(D' =-u6Bdiamond(in)*<3<*pgD9' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*p%(D' =-u6Bdiamond(in)*<3<*p+"0 tY(  t t  x$0e0e?Rectangle 2 `}   EAVN   t  xD0e0e?Rectangle 3 `  <Most common site of AVN Femoral head Humeral head Knee Small joints of hands and feet Most common orthopedic complication in SCD and occurs in up to 50% of all pt SCD is the most common cause of AVN in children< > } >} H t 0޽h ? ff>>\`Y{ff___PPT10i.p+D=' = @B +"0 xW(  x x  x 0e0e?Rectangle 2 `}   HStroke   x  xh0e0e?Rectangle 3 `  7Stroke occurs in 7-11% of children with SCD SCD-SS overall risk of stroke 3.75% throughout lifetime <2 yrs have lowest incidence of stroke 2-5 years have highest incidence infarctive stroke 20-29 years have highest incidence hemorrhagic stroke Z H x 0޽h ? ff>>\`Y{ff___PPT10i.n"+D=' = @B +"0 qi|(  | |  x!0e0e?Rectangle 2 `}   K Questions    |  x$0e0e?Rectangle 3"PK![Content_Types].xml|N0 HC+jS8 @:Q۸ ??\o<7p]V޷O(I'6E=, ){Ō4>I)q7UuDހǏ)}nL"Mᴸ&g0eSA)΄2';2 WYu7{ɯΒzŘqFrj9K*(]mOlPK!Z,[ _rels/.relslj0 ``t_Pƈ[>,dgzjǎ?I'f#®Pb-\/Ƿ0Z]nLnp__3.iJV KQBiDžrL,Vʌ/7р4`ANar+m;E/'3U Aںv83/PK!e[drs/downrev.xmlDN@M|͘x'[J?&$P`m;쮴/|'l1VƲ(A\ZpXMAL .a1am{:B%"} \J_dЏlGuCaᦕiobUɶ{WfX>4:-WW޴Iec5z>Sm49PK-![Content_Types].xmlPK-!Z,[ _rels/.relsPK-!e[drs/downrev.xmlPK `H$D 0  What is the most common cause of osteomyelitis in pt with SCD-SS? Salmonella #1, S. aureus #2 How much does Hb usually drop with aplastic crisis? >= 30% reduction from baseline Hb What is the most common cause of aplastic crisis? Parvovirus B19 causes ~70% B Z Z5 Z" Z2 Z ZB5"2   H | 0޽h ? ff>>\`Y{ff___PPT10.+qZDh' = @B D#' = @BA?%,( < +O%,( < +Dn' =%(D' =%(D' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*|B^%(D' =+4 8?\CB#ppt_xBCB#ppt_xB*Y3>B ppt_x<*|B^D' =+4 8?dCB1+#ppt_h/2BCB#ppt_yB*Y3>B ppt_y<*|B^Dn' =%(D' =%(D' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*|%(D' =+4 8?\CB#ppt_xBCB#ppt_xB*Y3>B ppt_x<*|D' =+4 8?dCB1+#ppt_h/2BCB#ppt_yB*Y3>B ppt_y<*|Dn' =%(D' =%(D' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*|%(D' =+4 8?\CB#ppt_xBCB#ppt_xB*Y3>B ppt_x<*|D' =+4 8?dCB1+#ppt_h/2BCB#ppt_yB*Y3>B ppt_y<*|+"K$0 U(  !   xC0e0e?Rectangle 2 `}   UBacterial infection     xF0e0e?Rectangle 3"PK![Content_Types].xml|N0 HC+jS8 @:Q۸ ??\o<7p]V޷O(I'6E=, ){Ō4>I)q7UuDހǏ)}nL"Mᴸ&g0eSA)΄2';2 WYu7{ɯΒzŘqFrj9K*(]mOlPK!Z,[ _rels/.relslj0 ``t_Pƈ[>,dgzjǎ?I'f#®Pb-\/Ƿ0Z]nLnp__3.iJV KQBiDžrL,Vʌ/7р4`ANar+m;E/'3U Aںv83/PK!%Sdrs/downrev.xmlDMK@Eax;;_RE $Qp̼&̛03wp˽˙-FӋ9YV0$ k;nV {ˤ@]!sTІ0R%~bm3btnzy$`ŁV-_Q0UV*{i>ѿ<+uz2.oA_z .7Y bpp.r _ ?PK-![Content_Types].xmlPK-!Z,[ _rels/.relsPK-!%Sdrs/downrev.xmlPK `H$D 0  What are most common bacteria causing infxn in SCD-SS? Streptococcus pneumoniae Staphylococcus aureus Salmonella species Haemophilus influenza type b Escherichia coli Klebsiella species*7  7 H  0޽h ? ff>>\`Y{ff___PPT10.n 5+qZD' = @B D' = @BA?%,( < +O%,( < +Dn' =%(D' =%(D' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*7P%(D' =+4 8?\CB#ppt_xBCB#ppt_xB*Y3>B ppt_x<*7PD' =+4 8?dCB1+#ppt_h/2BCB#ppt_yB*Y3>B ppt_y<*7PDn' =%(D' =%(D' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*Pf%(D' =+4 8?\CB#ppt_xBCB#ppt_xB*Y3>B ppt_x<*PfD' =+4 8?dCB1+#ppt_h/2BCB#ppt_yB*Y3>B ppt_y<*PfDn' =%(D' =%(D' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*fy%(D' =+4 8?\CB#ppt_xBCB#ppt_xB*Y3>B ppt_x<*fyD' =+4 8?dCB1+#ppt_h/2BCB#ppt_yB*Y3>B ppt_y<*fyDn' =%(D' =%(D' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*y%(D' =+4 8?\CB#ppt_xBCB#ppt_xB*Y3>B ppt_x<*yD' =+4 8?dCB1+#ppt_h/2BCB#ppt_yB*Y3>B ppt_y<*yDn' =%(D' =%(D' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*%(D' =+4 8?\CB#ppt_xBCB#ppt_xB*Y3>B ppt_x<*D' =+4 8?dCB1+#ppt_h/2BCB#ppt_yB*Y3>B ppt_y<*Dn' =%(D' =%(D' =4@BBBB%(D' =1:Bvisible*o3>+B#style.visibility<*%(D' =+4 8?\CB#ppt_xBCB#ppt_xB*Y3>B ppt_x<*D' =+4 8?dCB1+#ppt_h/2BCB#ppt_yB*Y3>B ppt_y<*+"0 r(     xhV0e0e?Rectangle 2 `}   O Complications     xY0e0e?Rectangle 3 `  KqAirway/Breathing Acute chest syndrome Chronic Pulmonary Hypertension CNS Stroke Pain Cardiovascular Hypertension  P4 P P  P P  P P4   rH  0޽h ? ff>>\`Y{ff___PPT10i. +D=' = @B +"0 s(     xw0e0e?Rectangle 2 `}   RGI Complications     x {0e0e?Rectangle 30P  I+GI Cholelithiasis, Choledocholithiasis, Acute Cholecystitis Abdominal Pain Crisis Sickle Hepatopathy Pancreatitis Peptic Ulcer Disease Hematologic Acute splenic sequestration crisis Aplastic crisis Blood transfusion complications GU/Gyn Priapism Pregnancy Complications, need for Genetic Counseling  P9 P) " P  P3 P  Z P> P b" 3    > ,H  0޽h ? ff>>\`Y{ff___PPT10i.ppO+D=' = @B +"=0 D<(     x0e0e?Rectangle 2 `}   O Complications  y   x0e0e?Rectangle 3 `  Infection Osteomyelitis Renal Disease Orthopedic Aseptic Necrosis of the hip (AVN) Chronic Leg Ulcers Multiple Organ Failure Syndrome: fever, decrease Hb, decrease plt, rhabdomyolysis, mental status changes   P P P5 Z# PH P Z 5#H H  0޽h ? ff>>\`Y{ff___PPT10i.DM+D=' = @B +"#0 *"(     xd0e0e?Rectangle 2 `}   N Bibliography   `   xD0e0e?Rectangle 3 `  NKoshy, M and Dorn, L.  Continuing Care for Adult Patients with Sickle Cell Disease. Hematology/Oncology Clinics of North America 1996; 10 (6): 1265-1273. Lottenberg, R and Hassell, K.  An Evidence-Based Approach to the Treatment of Adults with Sickle Cell Disease. Hematology 2005; 58-65. Mehta, S et al.  Opportunities to Improve Outcomes in Sickle Cell Disease. American Family Physician 2006; 74 (2): 303-310. Z H  0޽h ? ff>>\`Y{ff___PPT10i.PB+D=' = @B +"m0 tl(     p0e0e?Title 1 `}   N Bibliography      0e0e?,Content Placeholder 2 `  Redding-Lallinger, R and Knoll, C.  Sickle Cell Disease Pathophysiology and Treatment. Curr Probl Pediatr Adolesc Health Care 2006; 36: 346-376. Wethers, D.  Sickle Cell Disease in Childhood: Part I. Laboratory Diagnosis, Pathophysiology and Health Maintenance. American Family Physician 2000; 62 (5): 1013-1020. F F FH  0޽h ? ff>>\`Y{ff___PPT10i.RT|+D=' = @B +"g0 nf(     p0e0e?Title 1 `}   N Bibliography      0e0e?,Content Placeholder 2 `  Wethers, D.  Sickle Cell Disease in Childhood: Part II. Diagnosis and Treatment of Major Complications and Recent Advances in Treatment. American Family Physician 2000; 62 (6): 1309-1314.   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   !On-screen ShowHCHD%' (ArialCalibriDefault Design?Sickle Cell Disease: Outpatient Management and ComplicationsSickle Cell Disease Hemoglobin S VariantsAverage LifespanPrenatal or PreconceptionBirth-6 months6 months-2 years2 years2 years-5 years >5 yearsGrowth AdolescenceAdult PneumovaxBlood PressurePulmonary HypertensionPCN VK prophylaxis HydroxyureaBlood TransfusionClinical Case #1Clinical Case #1Clinical Case #1Clinical Case #2Clinical Case #2Clinical Case #3DDX Limp in Hb SS DiseaseAVNStroke QuestionsBacterial infectionComplicationsGI ComplicationsComplications Bibliography Bibliography Bibliography  Fonts UsedDesign Template Slide Titles%_anoopaanoopa  !"#$%&'()*+,-./0123456789:;<=>?@ABCDEFGHIJKLMNOPQRSTUVWXYZ[\]^_`abcdefghijklmnopqrstuvwxyz{|}~      !"#$%&'()*+,-./0123456789:;<=>?@ABCDEFGHIJKLMNOPQRSTUVWXYZ[\]^_`abcdefghijklmnopqrstuvwxyz{|}~      !"#$%&'()*+,-./0123456789:;<=>?@ABCDEFGHIJKLMNOPQRSTUVWXYZ[\]^_`abcdefghjklmnopqrstuvwxyz{|}~      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