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Y ESummary of ArtifactsCase #1Newborn infant (term twin B) with the following indices Hgb 10.2 Hct 33.2 MCV 94.8 RDW 14.0 RBC 3.5 M Could this be iron deficiency anemia? Why or why not?<8P1P8 P8i,8]Iron deficiency in newbornMost likely due to blood loss, such as twin-twin transfusion Newborn infants will take all the iron that they need from mother even if mother is iron deficient Average amount of iron in body at birth is 250 mg (80 ppm) At 6 months iron concentration will decrease to 60 ppm and infant becomes at risk for iron deficiency, especially if not taking iron-enriched foods or formula Remember to supplement exclusively breast-fed babies at six months with iron 0ZZZ,56Impact of iron deficiency anemia on mental development77In one study, infants with Hgb < 9.5 at 8 mos had decreased locomotor and hand-eye coordination Infants with low ferritin levels, later had decreased language ability, and a 3.3 times increase in the odds of having an IQ < 70 by age 5P  -r Case # 2You are given the following CBC from a newborn African-American male infant: Hb 14.9 MCV 93 MCH 31 MCHC 33 RDW 14 RBC 5.7 Retic 4 Platelets 220 Spleen 1 cm T bili 8.9, day 3 What is your diagnosis, if any? ^MZaZ ZZMa   >M+.  Alpha thalassemia   Predominant hemoglobin at birth is hemoglobin F composed of alpha and gamma chains Hemoglobin A consisting of alpha and beta chains is not predominant until 6 months of life Iron deficiency is not present at birth Therefore, low MCV (<98) at birth is almost always due to alpha thalassemia In African Americans is almost always benign, consisting of single gene deletion (1 of 4) In Asians, however, may be more serious with multiple gene deletions. Should be investigated. May be only opportunity to easily detect alpha thalassemia since after 6 months, can only detect beta thalassemia on HgB electrophoresis (elevated hemoglobin A2). Would need to do genetic studies to discover alpha thal.Pb  , _ What is a low MCV?= By age 1 lower limit of normal MCV = Age (yrs) + 70$Z=Z> Case #3Newborn Caucasian baby boy, born via C-section HgB 17 MCV 107 MCH 32 MCHC 33 RDW 14 RBC 5.3 Retic 4 Platelets 220 Spleen not palpable Infant pale HR 200, weak pulses.1Z{Z1{,1-F  Blood lossOBaby had bled out during delivery Not hemodiluted yet Needs circulatory support&   Case #49 month old Caucasian boy. Hb 9.7 MCV 76 MCH 33 MCHC 38 RDW 18 RBC 4.7 Retic 8% Platelets 340 Spleen 1 cm palpable Bilirubin 18.7 on day of life 3 What is going on?J 3o  >+' *Hereditary Spherocytosis fCaused by loss of spectrin and/or ankyrin giving cytoskeletal instability and surface area loss Best test is osmotic fragility test When MCHC is high, gives perspective on surface area to volume of cells. Highest when spheres present. Other possible diagnostic use of MCHC is with autoimmune hemolytic anemia which causes the generation of microspherocytesggP Case #518 month old Caucasian male with Tetralogy of Fallot Hb 17.2 MCV 66 MCH 30 MCHC 32 RDW 17 RBC 5.8 Retic 1.7 Platelets 110 Spleen palpable 2 cm What is the diagnosis and what does this child need? F5Z]Z6Z5]6P! -_+Fe deficiency in patients with polycythemia,, Needs iron or will stroke out!!! Iron deficiency state gives higher viscosity Combination of polycythemia and iron deficiency can cause stroke ^ ' Case #6You are following a 16 year old male who is a top-notch cross-country runner, who has been feeling tired and not up to par this year His indices are: Hgb = 11.7 Hct = 35% MCV = 80 MCH = 28.9 RDW = 16 What is your diagnosis and why?FZ2Z Z2 ,D jJogger s anemia and anemia of highly-trained athletes66Boyadijev N. et al: Br J Sports Med 34:200-204, 2000. Compared indices of highly trained pubescent athletes with controls Athletes had lower HgB, RBC count, and MCV than controls Additionally, there is a phenomenom called  runner s anemia with blood loss from continued microtrauma, usually asx, but may have increased fatigue Get plasma expansion with running and hemolysis from pounding of feet on pavement and hemoglobinuria Should be considered when mild anemia is well-tolerated by an avid runner but may be symptomatic FHZZZH~ < 9  G 'cUse of MCV and RDWMCV ! RDW ! Fe deficiency PPV = 97.8% Best test for IDA is CHr (concentration of HgB in reticulocytes), not yet generally available but coming soon Trial of iron can be used as diagnostic tool with 2-3 mg/kg/d of elemental iron (FeSO4 is 20% elemental) Should see retics increasing in 48-72 hours HgB will increase at 0.2-0.3 g/dl per day in first 3 weeks MCV ! RDW nl Thalassemia trait MCV nl RDW nl Acute anemia/chronic intercurrent illness Transient erythrocytopenia (TEC) MCV nl RDW ! 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